AL amyloidosis

From BugSigDB


AL Amyloidosis is a plasma cell disorder characterized by the aggregation and deposition of insoluble amyloid fibrils derived from misfolding of monoclonal immunoglobulin light chains usually produced by a plasma cell tumor (see this term). It usually presents as primary systemic amyloidosis (PSA) with multiple organ involvement and less frequently as primary localized amyloidosis (PLA; see these terms) restricted to a single organ.
Aliases
  • AL amyloidosis
  • amyloidosis AL
  • amyloidosis primary systemic
  • Immunoglobulinic amyloidosis
  • Light chain amyloidosis
  • Light-chain amyloidosis
  • primary AL amyloidosis
  • Primary amyloidosis
  • primary amyloidosis
  • primary amyloidosis (formerly)
  • primary systemic AL amyloidosis
  • primary systemic amyloidosis
  • systemic AL amyloidosis
  • systemic AL amyloidsis
  • Systemic monoclonal immunoglobulin light chain amyloidosis