Body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency
From BugSigDB
Body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency is a very rare genetic skin disease characterized by severe skin laxity affecting the trunk and limbs.
- Aliases
- body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency
- pseudoxanthoma elasticum-like disorder with multiple coagulation factor deficiency
- Pseudoxanthoma elasticum-like syndrome
- pseudoxanthoma elasticum-like syndrome
- PXE-like disorder with multiple coagulation Factor deficiency
- PXE-like syndrome