Body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency

From BugSigDB


Body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency is a very rare genetic skin disease characterized by severe skin laxity affecting the trunk and limbs.
Aliases
  • body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency
  • pseudoxanthoma elasticum-like disorder with multiple coagulation factor deficiency
  • Pseudoxanthoma elasticum-like syndrome
  • pseudoxanthoma elasticum-like syndrome
  • PXE-like disorder with multiple coagulation Factor deficiency
  • PXE-like syndrome